Skip to content
2000
Volume 21, Issue 1
  • ISSN: 1573-4056
  • E-ISSN: 1875-6603

Abstract

Introduction

Cor Triatriatum Sinister (CTS) is a rare congenital anomaly, accounting for 0.1%- 0.4% of congenital heart diseases. While often diagnosed and treated in infancy, some cases remain asymptomatic until adulthood due to large fenestrations. This report presents a unique case of CTS in an adult coexisting with chronic adhesive pericarditis, which may have contributed to chronic atrial dilatation, a condition not previously documented.

Case Presentation

A 60-year-old asymptomatic Taiwanese male underwent a routine medical examination. Coronary computed tomography angiography revealed a fenestrated septum dividing the left atrium, consistent with CTS. Virtual endoscopy confirmed two wide fenestrations. Notably, chronic adhesive pericarditis, evidenced by curvilinear calcifications, was diagnosed. This condition likely exacerbated the hemodynamic impact of CTS, contributing to left atrial dilation and atrial fibrillation. Atrial fibrillation was identified, and the patient was treated with an anticoagulant for stroke prevention.

Conclusion

This is the first reported case of CTS coexisting with chronic adhesive pericarditis. Advanced imaging modalities, including cardiac computed tomography, angiography, and virtual endoscopy, are crucial for diagnosis and anatomical evaluation. Chronic adhesive pericarditis may amplify the effects of CTS, leading to complications, including atrial fibrillation. Anticoagulation is essential for stroke prevention in such cases.

This is an open access article distributed under the terms of the Creative Commons Attribution 4.0 International Public License (CC-BY 4.0), a copy of which is available at: https://creativecommons.org/licenses/by/4.0/legalcode. This license permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Loading

Article metrics loading...

/content/journals/cmir/10.2174/0115734056383803250523070650
2025-06-03
2025-10-06
Loading full text...

Full text loading...

/deliver/fulltext/cmir/21/1/CMIR-21-E15734056383803.html?itemId=/content/journals/cmir/10.2174/0115734056383803250523070650&mimeType=html&fmt=ahah

References

  1. SzaboT.M. HeidenhofferE. KirchmaierÁ. PelokB. FrigyA. Cor triatriatum sinister presenting as cardioembolic stroke in a young woman.Diagnostics20221319710.3390/diagnostics13010097
    [Google Scholar]
  2. DoyleJ.F. Cor triatriatum in a young woman with syncope.BMJ Case Rep.20112011bcr012011374810.1136/bcr.01.2011.374822707656
    [Google Scholar]
  3. OliveiraT.A. MarquioriR.A.S. A rare case of cor triatriatum sinister in adulthood with atypical manifestation.Heart Int.2020141535510.17925/HI.2020.14.1.53
    [Google Scholar]
  4. DiestroJ.D.B. RegaldoJ.J.H. GonzalesE.M. DorotanM.K.C. EspirituA.I. PascualJ.L.R. Cor triatriatum and stroke.BMJ Case Rep.20172017bcr-2017-21976310.1136/bcr‑2017‑219763
    [Google Scholar]
  5. KerJ. Cor triatriatum sinister presenting with adult onset atrial fibrillation—Another rare cause for a common clinical problem.Int. J. Cardiol.20131671e12e1310.1016/j.ijcard.2013.01.269
    [Google Scholar]
  6. ZepedaI.A. MorcosP. CastellanosL.R. Cor triatriatum sinister identified after new onset atrial fibrillation in an elderly man.Case Rep. Med.201420141510.1155/2014/674018
    [Google Scholar]
  7. RodefeldM.D. BrownJ.W. HeimansohnD.A. KingH. GirodD.A. HurwitzR.A. CaldwellR.L. Cor triatriatum: Clinical presentation and surgical results in 12 patients.Ann. Thorac. Surg.199050456256810.1016/0003‑4975(90)90190‑H
    [Google Scholar]
  8. Marín-GarcíaJ. TandonR. LucasR.V.Jr EdwardsJ.E. Cor triatriatum: Study of 20 cases.Am. J. Cardiol.1975351596610.1016/0002‑9149(75)90559‑7
    [Google Scholar]
  9. JhaA.K. MakhijaN. Cor triatriatum: A review.Semin. Cardiothorac. Vasc. Anesth.201721217818510.1177/1089253216680495
    [Google Scholar]
  10. GoelA. ViswamitraS. ReddyB.N. GaduputiJ. Computed tomography features of cor triatriatum: An institutional review.Br. J. Radiol.20219411192020125210.1259/bjr.20201252
    [Google Scholar]
  11. BezginT. ÇangaY. KaragözA. YılmazF. DoğanC. ElveranA. KaymazC. Multimodality imaging of cor triatriatum sinister in an octagenerian.Echocardiography2014318E254E25610.1111/echo.12660
    [Google Scholar]
  12. SchlÜterM. LangensteinB.A. ThierW. SchmiegelW-H. KrebberH-J. KalmarP. HanrathP. Transesophageal two-dimensional echocardiography in the diagnosis of cor triatriatum in the adult.J. Am. Coll. Cardiol.1983251011101510.1016/S0735‑1097(83)80252‑6
    [Google Scholar]
  13. SuC.S. Usefulness of multidetector-row computed tomography in evaluating adult cor triatriatum.Tex. Heart Inst. J.2008353349351
    [Google Scholar]
  14. AlaloolaA.A. AlghamdiR. ArafatA.A. Do we really need a new classification for cor triatriatum sinister?J. Card. Surg.202237124534453510.1111/jocs.17031
    [Google Scholar]
  15. ThakrarA. ShapiroM.D. JassalD.S. NeilanT.G. KingM.E.E. AbbaraS. Cor triatriatum: The utility of cardiovascular imaging.Can. J. Cardiol.200723214314510.1016/S0828‑282X(07)70735‑3
    [Google Scholar]
  16. LoefflerE. Unusual malformation of the left atrium; Pulmonary sinus.Arch. Pathol.1949485371376
    [Google Scholar]
  17. ThamJ.L. PuppalaS. Cor triatriatum sinistrum.Radiology20233083e23124610.1148/radiol.231246
    [Google Scholar]
  18. NassarP.N. HamdanR.H. Cor triatriatum sinistrum: Classification and imaging modalities.Eur. J. Cardiovasc. Med.20111111848710.5083/ejcm.20424884.21
    [Google Scholar]
  19. GharagozlooF. BulkleyB.H. HutchinsG.M. A proposed pathogenesis of cor triatriatum: Impingement of the left superior vena cava on the developing left atrium.Am. Heart J.197794561862610.1016/S0002‑8703(77)80132‑4
    [Google Scholar]
  20. SabriA.R.A. JoshiN. KindiH.A. SenaidiK.S.A. Cor triatriatum sinistrum.Sultan Qaboos Univ. Med. J.2021212e324e32610.18295/squmj.2021.21.02.026
    [Google Scholar]
  21. KaplanJ. YelamanchiliV. KanwalA. HunyadiV. IanitelliM.M. Cor triatriatum dexter: A rare congenital malformation found on transesophageal echocardiogram.J. Am. Coll. Cardiol.2022799316710.1016/S0735‑1097(22)04158‑4
    [Google Scholar]
  22. NguyenT. PhillipsC. MovahedA. Incidental findings of pericardial calcification.World J. Clin. Cases20142945545810.12998/wjcc.v2.i9.455
    [Google Scholar]
  23. McMurrayC. CaperD. CornatzerW.E. Chronic adhesive, pericarditis due to the rheumatic state, associated with liver damage, serous effusions, and pigmentation.Gastroenterology195117229430310.1016/S0016‑5085(51)80107‑0
    [Google Scholar]
  24. SpengosK. GialafosE. VassilopoulouS. Ischemic stroke as an uncommon complication of Cor triatriatum.J. Stroke Cerebrovasc. Dis.200817643643810.1016/j.jstrokecerebrovasdis.2008.07.007
    [Google Scholar]
/content/journals/cmir/10.2174/0115734056383803250523070650
Loading
/content/journals/cmir/10.2174/0115734056383803250523070650
Loading

Data & Media loading...

This is a required field
Please enter a valid email address
Approval was a Success
Invalid data
An Error Occurred
Approval was partially successful, following selected items could not be processed due to error
Please enter a valid_number test